Chen C P, Liu F F, Jan S W, Wang K G, Lan C C
Department of Obstetrics and Gynecology, Mackay Memorial Hospital, Taipei, Taiwan, Republic of China.
Am J Perinatol. 1997 Jan;14(1):31-3. doi: 10.1055/s-2007-994092.
We describe the first report of distal obstructive uropathy and prune-belly syndrome in an infant with amniotic band syndrome. Prenatal ultrasonographic examination in the third trimester revealed intermittent oligohydramnios, bilateral hydronephrosis, and megacystis. Postnatally, the infant was found to have a scalp defect, a skin pedicle, pseudosyndactyly and constriction rings on the hands, marked distention of the abdomen, a fibrous band attached to the proximal urethra causing urethral stricture, a swollen penile shaft, bilateral talipes equinovarus, and syndactyly of the feet. Multiple fibrous amniotic bands could be identified in the placenta. Our case shows that fetal distal obstructive uropathy can be associated with the congenital constriction band syndrome.
我们报告了首例患有羊膜带综合征的婴儿出现远端梗阻性尿路病和梅干腹综合征的病例。孕晚期产前超声检查发现间歇性羊水过少、双侧肾积水和巨大膀胱。出生后，该婴儿被发现有头皮缺损、皮肤蒂、手部假性并指和缩窄环、腹部明显膨隆、一条附着于近端尿道导致尿道狭窄的纤维带、阴茎肿胀、双侧马蹄内翻足和足部并指。在胎盘中可识别出多条纤维性羊膜带。我们的病例表明，胎儿远端梗阻性尿路病可能与先天性缩窄带综合征有关。
