Grimes Adrian C, Erwin Kyle N, Stadt Harriett A, Hunter Ginger L, Gefroh Holly A, Tsai Huai-Jen, Kirby Margaret L
Department of Molecular and Cellular Biology and Pathobiology, Medical University of South Carolina, Charleston, South Carolina 29425, USA.
Toxicol Sci. 2008 Nov;106(1):193-205. doi: 10.1093/toxsci/kfn154. Epub 2008 Jul 26.
We have used zebrafish and 3,3',4,4',5-pentachlorobiphenyl (PCB126) to investigate the developmental toxicity of polychlorinated biphenyls (PCBs) that exert their effects through the aryl hydrocarbon receptor (AHR). We found that cardiac and neural crest (NC)-derived jaw and branchial cartilages are specifically targeted early in development. The suite of malformations, which ultimately leads to circulatory failure, includes a severely dysmorphic heart with a reduced bulbus arteriosus and abnormal atrioventricular and outflow valve formation. Early NC migration and patterning of the jaw and branchial cartilages was normal. However, the jaw and branchial cartilages failed to grow to normal size. In the heart, the ventricular myocardium showed a reduction in cell number and size. The heart and jaw/branchial phenotype could be rescued by pifithrin-alpha, a blocker of p53. However, the function of pifithrin-alpha in this model may act as a competitive inhibitor of PCB at the AHR and is likely independent of p53. Morpholinos against p53 did not rescue the phenotype, nor were zebrafish with a mutant p53-null allele resistant to PCB126 toxicity. Morpholino knockdown of cardiac troponin T, which blocks the onset of cardiac function, prevented the PCB126-induced cardiac dysmorphogenesis but not the jaw/branchial phenotype. The cardiovascular characteristics appear to be similar to hypoplastic left heart syndrome (HLHS) and introduce the potential of zebrafish as a model to study this environmentally induced cardiovascular malformation. HLHS is a severe congenital cardiovascular malformation that has previously been linked to industrial releases of dioxins and PCBs.
我们利用斑马鱼和3,3',4,4',5-五氯联苯(PCB126)来研究多氯联苯(PCBs)通过芳烃受体(AHR)发挥作用时的发育毒性。我们发现,心脏以及神经嵴(NC)衍生的颌骨和鳃软骨在发育早期会受到特异性影响。一系列最终导致循环衰竭的畸形包括严重畸形的心脏,其动脉球减少,房室和流出瓣膜形成异常。早期NC迁移以及颌骨和鳃软骨的模式正常。然而,颌骨和鳃软骨未能生长到正常大小。在心脏中,心室心肌细胞数量和大小减少。心脏和颌骨/鳃的表型可以被p53的阻滞剂pifithrin-α挽救。然而,pifithrin-α在该模型中的功能可能是作为AHR处PCB的竞争性抑制剂,并且可能独立于p53。针对p53的吗啉代寡核苷酸不能挽救该表型,p53基因缺失突变的斑马鱼对PCB126毒性也没有抗性。对心肌肌钙蛋白T进行吗啉代敲低可阻断心脏功能的起始,从而防止PCB126诱导的心脏畸形发生,但不能防止颌骨/鳃的表型出现。这些心血管特征似乎与左心发育不全综合征(HLHS)相似,并表明斑马鱼作为研究这种环境诱导的心血管畸形模型的潜力。HLHS是一种严重的先天性心血管畸形,此前已与二恶英和PCBs的工业排放有关。