Teunissen B, Cremers C W
Institute of Otorhinolaryngology, University Hospital of Nijmegen, The Netherlands.
Int J Pediatr Otorhinolaryngol. 1991 May;21(3):217-26. doi: 10.1016/0165-5876(91)90003-t.
The surgical findings and results are presented on 32 ears with congenital stapes ankylosis with an associated congenital anomaly of the ossicular chain. One third of the patients had a syndromal diagnosis. In 26 ears, stapedectomy could be performed. In 2 other ears, stapes ankylosis to the bony facial canal was mobilized successfully. In the 4 remaining ears, surgical intervention had to be limited to an exploratory tympanotomy for various reasons. The average hearing gain was 23 dB for the 28 ears on which stapes surgery had been performed. A substantial hearing gain of at least 15 dB was achieved in 19 of these 28 ears (68%). The end result was limited to a small extent by an average preoperative sensorineural component of 16 dB in the hearing loss. A review of the findings and results from other larger series in the literature are presented.
本文报告了32例先天性镫骨固定并伴有听骨链先天性异常患者的手术发现及结果。三分之一的患者有综合征诊断。26耳可行镫骨切除术。另外2耳镫骨与骨面神经管的固定成功松解。其余4耳因各种原因手术干预仅限于探查性鼓室切开术。接受镫骨手术的28耳平均听力增益为23dB。这28耳中有19耳（68%）听力显著增益至少15dB。最终结果在一定程度上受平均术前感音神经性听力损失16dB的限制。文中还回顾了文献中其他较大系列研究的发现及结果。
