Sturm J, Raute M, Trede M
Chirurgische Klinik, Universität Heidelberg, Mannheim, Bundesrepublik Deutschland.
Langenbecks Arch Chir. 1991;376(3):182-8. doi: 10.1007/BF00250345.
The leiomyosarcoma of vascular origin is a very rare tumor which is rarely recovered before the disease has reached an advanced stage because of non-specific and late symptoms. This is a report of 3 cases with leiomyosarcoma of the vena cava and a review of the literature. A high local recurrence rate and high frequency of distant metastases are responsible for the bad long-term prognosis. Early hematogenous tumor spread is favored by intraluminal tumor growth. Only complete surgical resection--if necessary with vascular reconstruction--can improve the bad long-term prognosis.
血管源性平滑肌肉瘤是一种非常罕见的肿瘤，由于症状不典型且出现较晚，在疾病发展到晚期之前很少能被发现。本文报告了3例腔静脉平滑肌肉瘤病例并复习相关文献。局部复发率高和远处转移频繁导致其长期预后不良。腔内肿瘤生长有利于肿瘤早期血行播散。只有完整的手术切除——必要时进行血管重建——才能改善其不良的长期预后。
