Betend T B, brunat M, David L, Lesbros F, Hermier M
Arch Fr Pediatr. 1976 Aug-Sep;33(7):683-91.
A nephroblastoma occurred in the evolution of a case of Beckwith's syndrome. This rare association is not fortuitous. The bifocal character of the tumor is noted for the first time in the Beckwith's syndrome; however, it has already been observed in other conditions, which are known to promote the development of nephroblastomas. Wilm's tumor is only one of the tumors which may be associated with Beckwith's syndrome. These morbid associations and certain histological features bring together some material for the understanding of the nature of the histo-genetic relationship between different aspects of constitutional pathology and tumors.
肾母细胞瘤发生于1例贝克威思综合征的病程中。这种罕见的关联并非偶然。在贝克威思综合征中首次发现肿瘤具有双灶性特征；然而，在已知会促进肾母细胞瘤发生发展的其他情况下也已观察到这种情况。威尔姆斯瘤只是可能与贝克威思综合征相关的肿瘤之一。这些病态关联和某些组织学特征为理解体质病理学不同方面与肿瘤之间组织发生学关系的本质提供了一些资料。
