Javangula Kalyana C, O'Regan David J
Division of Cardiothoracic Surgery, Yorkshire Heart Centre, Leeds General Infirmary, Leeds, England.
Ann Thorac Surg. 2008 Sep;86(3):1008-11. doi: 10.1016/j.athoracsur.2008.02.069.
We report the case of a 43-year-old woman with a history of alveolar rhabdomyosarcoma of the forearm, scalp, and paraspinal region who developed acute shortness of breath owing to a tumor arising from the left atrium and extending through the coronary sinus. This was causing partial obstruction across the tricuspid valve as a result of the ball-valve effect. Emergency resection of the atrial mass was performed, and histologic analysis confirmed the presence of metastatic rhabdomyosarcoma. To our knowledge, this is the first reported case of emergency surgical resection of intracardiac metastatic alveolar rhabdomyosarcoma.
我们报告了一名43岁女性的病例,该患者有前臂、头皮和椎旁区域的肺泡横纹肌肉瘤病史,因左心房肿瘤并延伸至冠状窦而出现急性呼吸急促。由于球阀效应,这导致三尖瓣出现部分梗阻。对心房肿块进行了急诊切除,组织学分析证实存在转移性横纹肌肉瘤。据我们所知,这是首例报告的心脏内转移性肺泡横纹肌肉瘤急诊手术切除病例。