Stjernholm C, Muren C, Bredberg G
Karolinska Institutet, Department of Radiology at Stockholm Söder Hospital, 118 83 Stockholm, Sweden.
Cochlear Implants Int. 2001 Mar;2(1):59-71. doi: 10.1179/cim.2001.2.1.59.
Children with CHARGE have multiple disabilities. Impairments of vision and hearing, balance problems and facial palsy are common. Few reports have dealt with their radiological temporal bone changes and none with cochlear implant surgery. The pre-operative temporal bone computed tomography (CT) and surgical findings of one child with CHARGE and one with a CHARGE-like condition who have received cochlear implants are reported. The findings include absent semicircular canals, narrow orifice for the cochlear nerve, and abnormalities of the oval and round window, the facial canal and the ossicles. CT can be used as a diagnostic tool as these combinations of temporal bone changes are extremely rare in other materials. Cochlear implants may help these often very isolated children to communicate.
患有CHARGE综合征的儿童存在多种残疾。视力和听力障碍、平衡问题及面瘫很常见。关于他们颞骨的放射学改变的报道很少，而关于人工耳蜗植入手术的报道则没有。本文报告了一名患有CHARGE综合征和一名患有类似CHARGE综合征的儿童在接受人工耳蜗植入术前的颞骨计算机断层扫描（CT）及手术结果。结果包括半规管缺失、耳蜗神经孔狭窄、卵圆窗和圆窗、面神经管及听小骨异常。由于这些颞骨改变的组合在其他病例中极为罕见，CT可作为一种诊断工具。人工耳蜗植入可能有助于这些通常非常孤独的儿童进行交流。
