Dillon Brian J, Alomari Ahmad I
Division of Vascular and Interventional Radiology, Department of Radiology, The Children's Hospital Boston, Harvard Medical School, 300 Longwood Avenue, Boston, MA 02115, USA.
Surg Radiol Anat. 2009 Mar;31(3):215-9. doi: 10.1007/s00276-008-0411-9. Epub 2008 Sep 16.
Penoscrotal transposition (PST) is a rare congenital anomaly characterized by caudal location of the penis with respect to the scrotum. PST may be seen in isolation or associated with caudal regression syndrome. We present a case of an infant born with penoscrotal transposition, bladder agenesis, a solitary dysplastic kidney, and caudal regression. The patient developed anuria and was referred for angiography for preoperative planning for renal transplantation and genital reconstruction. Angiography demonstrated an aberrant abdominal umbilical artery, an anomaly classically associated with sirenomelia but also has been described in caudal regression.
阴茎阴囊转位(PST)是一种罕见的先天性异常,其特征是阴茎相对于阴囊位于尾侧。PST可单独出现或与尾侧退化综合征相关。我们报告一例出生时患有阴茎阴囊转位、膀胱缺如、孤立性发育不良肾和尾侧退化的婴儿病例。该患者出现无尿,因肾移植和生殖器重建的术前规划而转诊进行血管造影。血管造影显示一条异常的腹侧脐动脉,这种异常通常与并腿畸形相关,但也在尾侧退化中有所描述。