Abbes K, Khabir A, Bahloul K, Boudawara M Z, Boudawara T S
Laboratoire d'anatomie et de cytologie pathologique, CHU Habib-Bourguiba, route El-Aïn-Km-0,5, 3029 Sfax, Tunisie.
Neurochirurgie. 2009 Jun;55(3):333-6. doi: 10.1016/j.neuchi.2008.05.003. Epub 2008 Sep 19.
Choroid plexus carcinomas are rare and occur more frequently in children than in adults. The differential diagnosis includes choroid plexus papilloma and papillary ependymoma. The prognosis is generally poor. The objective of this paper is to discuss the epidemiological characteristics, diagnosis, treatment, and prognosis of this rare childhood tumor.
A three-year-old child was hospitalized with a history of partial epilepsy and intracranial hypertension. A computed tomography scan showed an intracranial mass measuring 11cm in diameter, extending to the ventricle system with heterogeneous contrast enhancement. He was urgently operated for loss of consciousness. During the operation, the patient developed an abundant hemorrhage and died. The histopathological examination of the excised tumor identified a choroid plexus carcinoma.
Choroid plexus carcinomas are rare and treatment is currently controversial. Radical excision is quite difficult and associated with excessive blood loss.
脉络丛癌罕见，在儿童中比在成人中更常见。鉴别诊断包括脉络丛乳头状瘤和乳头状室管膜瘤。其预后通常较差。本文的目的是探讨这种罕见儿童肿瘤的流行病学特征、诊断、治疗及预后。
一名三岁儿童因部分性癫痫和颅内高压病史入院。计算机断层扫描显示颅内有一个直径11厘米的肿块，延伸至脑室系统，增强扫描呈不均匀强化。因意识丧失他紧急接受了手术。术中，患者出现大量出血并死亡。对切除肿瘤的组织病理学检查确诊为脉络丛癌。
脉络丛癌罕见，目前治疗存在争议。根治性切除相当困难且伴有大量失血。
