Singh Harminder, Kalra Ravi, Keshavamurthy Ganapathi B, Singh Maninder, Singh Charanjit
Department of Cardiology, Military Hospital, Maharashtra, India.
Congenit Heart Dis. 2008 Sep-Oct;3(5):347-51. doi: 10.1111/j.1747-0803.2008.00179.x.
We report an 8-year-old child presenting with classical features of hypertrophic obstructive cardiomyopathy and Noonan syndrome with New York Heart Association (NYHA) class III symptoms. Due to progressively worsening symptoms, the child was taken up for percutaneous transluminal septal myocardial ablation, which was successfully performed. Postextrasystolic gradient fell down from 125 to 35 mm Hg. Other than postprocedure bifascicular block, no complications were encountered till 1 year of follow-up.
我们报告了一名8岁儿童,其表现出肥厚性梗阻性心肌病和努南综合征的典型特征,纽约心脏协会(NYHA)心功能分级为III级。由于症状逐渐恶化,该儿童接受了经皮腔内室间隔心肌消融术,手术成功进行。早搏后压差从125毫米汞柱降至35毫米汞柱。除术后双分支阻滞外,随访1年未出现其他并发症。