Zhou Fang, Liu Wenying, Tang Yunman
Department of Pediatric Surgery, West China Hospital, Sichuan University, Chengdu 610041, PR China.
J Pediatr Surg. 2008 Oct;43(10):1902-5. doi: 10.1016/j.jpedsurg.2008.06.005.
Poland syndrome is a constellation of anomalies including absent pectoralis muscle and rib defects, even with malformations of the upper extremity that more often affects boys than girls. This case describes a 5-year-old and 4-month-old girl diagnosed with Poland syndrome that required chest wall reconstruction. An autologous rib transplantation and terylene patch were used for repair of the chest wall defect. The girl had a satisfactory postoperative recovery. This technique was an effective method of treatment of this condition.
波兰综合征是一系列异常表现,包括胸大肌缺如和肋骨缺陷,甚至伴有上肢畸形,该病在男孩中的发病率高于女孩。本病例描述了一名5岁4个月大的女孩被诊断为波兰综合征,需要进行胸壁重建。采用自体肋骨移植和涤纶补片修复胸壁缺损。该女孩术后恢复良好。此技术是治疗该疾病的有效方法。