Khan Arif O
King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia.
J AAPOS. 2009 Feb;13(1):105-6. doi: 10.1016/j.jaapos.2008.07.011. Epub 2008 Oct 19.
Certain forms of congenital incomitant strabismus are associated with abnormal cranial nerve development and resultant abnormal orbital innervation (eg, Duane retraction syndrome, congenital fibrosis of the extraocular muscles [CFEOM]); such conditions can be considered congenital cranial dysinnervation disorders (CCDDs). In addition to duction limitation and/or ptosis, orbital CCDD phenotypes include inappropriate extraocular muscle and/or levator innervation by nerves intended for innervation of other structures (eg, some of the innervation intended for the medial rectus muscle inappropriately innervating the ipsilateral lateral rectus muscle in Duane retraction syndrome). This report documents a unique orbital dysinnervational pattern-supraduction during attempted adduction and infraduction during attempted abduction in the left affected eye of a girl with exotropia and enophthalmos.
某些形式的先天性非共同性斜视与颅神经发育异常及由此导致的眼眶神经支配异常有关（例如，杜安退缩综合征、眼外肌先天性纤维化[CFEOM]）；此类病症可被视为先天性颅神经支配障碍（CCDDs）。除了眼球运动受限和/或上睑下垂外，眼眶CCDD的表型还包括用于支配其他结构的神经对眼外肌和/或提上睑肌的不适当支配（例如，在杜安退缩综合征中，一些本应支配内直肌的神经不恰当地支配同侧外直肌）。本报告记录了一名患有外斜视和眼球内陷的女孩左眼在试图内收时出现上转、试图外展时出现下转这种独特的眼眶神经支配异常模式。
