Pratap Akshay, Tiwari Awadhesh, Pandey Sagar Raj, Agrawal Bikash, Paudel Gunraj, Adhikary Shailesh, Kumar Anand
Departments of Surgery, B.P. Koirala Institute of Health Sciences, Dharan, Nepal.
J Pediatr Urol. 2007 Aug;3(4):326-9. doi: 10.1016/j.jpurol.2006.10.010. Epub 2007 Feb 1.
We report the first case of cavernous hemangiolymphangioma of the urinary bladder without cutaneous hemangiomatosis. A 5-year-old boy was admitted for investigation of a 2-month episode of gross hematuria accompanied by lower abdominal pain. Radiological investigations revealed a solid enhancing mass at the dome of the bladder with associated low-flow lesion in the posterolateral wall of the bladder. Physical examination did not show any cutaneous vascular malformations. A differential diagnosis of hemangioma or rhabdomyosarcoma bladder was made, but fine-needle aspiration cytology did not reveal any malignant cells. At surgery, a red, wide-based, nodular tumor was found on the dome of the bladder and extending to the base and lateral walls. Partial cystectomy and excision of the cystic lymphangioma was performed. Histological examination of the resected specimen showed it to be a cavernous hemangiolymphangioma. The postoperative course was uneventful and no recurrence was seen after 8 months.
我们报告首例无皮肤血管瘤病的膀胱海绵状血管淋巴管瘤病例。一名5岁男孩因持续2个月的肉眼血尿伴下腹部疼痛入院检查。影像学检查显示膀胱顶部有一实性强化肿块，膀胱后壁有相关的低血流病变。体格检查未发现任何皮肤血管畸形。初步诊断为膀胱血管瘤或横纹肌肉瘤，但细针穿刺细胞学检查未发现任何恶性细胞。手术中，在膀胱顶部发现一个红色、宽基底、结节状肿瘤，肿瘤延伸至膀胱底部和侧壁。遂行部分膀胱切除术及囊性淋巴管瘤切除术。切除标本的组织学检查显示为海绵状血管淋巴管瘤。术后恢复顺利，8个月后未见复发。
