Daya Mahendra
Department of Plastic and Reconstructive Surgery, Nelson R Mandela School of Medicine, University of Kwazulu-Natal, Durban, South Africa.
Ann Plast Surg. 2008 Nov;61(5):549-51. doi: 10.1097/SAP.0b013e31816dd378.
Amniotic band syndrome (ABS) has an incidence of 1/15,000. Deformities vary from rare but bizarre craniofacial defects or truncal defects to the commoner limb defects. The pathogenesis of ABS remains controversial. The following is a case of a 3-month-old infant with amniotic band syndrome with the typical limb reduction defects, a constriction band on the thigh associated with a persistent sciatic artery and bifurcation of the femur and the duplication of the knee and tibia on the contra lateral side. The anatomy of the persistent sciatic artery is demonstrated in magnetic resonance angiography and digital subtraction angiography. The vascular anomaly was unilateral. The patient underwent surgical correction of the constriction band by excision and multiple Z plasty. This case is the first description of the coexistence of ABS and persistent sciatic artery. Persistent sciatic artery has angiographic incidence of 0.05%. Is this purely a coincidence? Or perhaps their coexistence may serve to further the understanding of the mechanism of ABS.
羊膜带综合征（ABS）的发病率为1/15000。畸形表现多样，从罕见但怪异的颅面缺陷或躯干缺陷到较常见的肢体缺陷。ABS的发病机制仍存在争议。以下是一例3个月大患有羊膜带综合征的婴儿，具有典型的肢体缩短缺陷、大腿上的束带并伴有持续坐骨动脉以及股骨分叉，对侧膝关节和胫骨重复。磁共振血管造影和数字减影血管造影显示了持续坐骨动脉的解剖结构。血管异常是单侧的。患者接受了束带切除及多次Z成形术的手术矫正。该病例是首次描述ABS与持续坐骨动脉并存。持续坐骨动脉的血管造影发病率为0.05%。这纯粹是巧合吗？或者它们的并存可能有助于进一步理解ABS的发病机制。
