伴有肝脏受累的淀粉样变性样肾小球病病例报告。
Case report of amyloidosis-like glomerulopathy with hepatic involvement.
作者信息
Ozawa K, Yamabe H, Fukushi K, Osawa H, Chiba N, Miyata M, Seino S, Inuma H, Sasaki T, Yoshikawa S
机构信息
Second Department of Internal Medicine, Hirosaki University School of Medicine, Japan.
出版信息
Nephron. 1991;58(3):347-50. doi: 10.1159/000186449.
A few cases of nephrotic syndrome with the glomerular deposition of an amyloid-like material which did not stain with Congo red have been documented. But extrarenal deposits have not been previously reported in this disease. We describe here a case of nephrotic syndrome associated with the deposition of an amyloid-like material in the liver as well as in the renal glomeruli. The deposits were made up of fibrillar structures which resembled those of amyloid when viewed through the electron microscope but they did not stain with Congo red. This is the first report of amyloidosis-like glomerulopathy with extrarenal deposits.
已有文献记载了几例肾小球沉积一种不被刚果红染色的淀粉样物质的肾病综合征病例。但此前尚未报道过该疾病的肾外沉积情况。我们在此描述一例肾病综合征，其肝脏以及肾小球中均有淀粉样物质沉积。这些沉积物由纤维状结构组成，通过电子显微镜观察时类似于淀粉样物质，但它们不被刚果红染色。这是首例伴有肾外沉积的淀粉样变性样肾小球病的报告。
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