Suppr超能文献

肌管性/核中心性肌病和中央轴空病

Myotubular/centronuclear myopathy and central core disease.

作者信息

Fujimura-Kiyono Chieko, Racz Gabor Z, Nishino Ichizo

机构信息

Department of Neuromuscular Research, National Institute of Neuroscience, National Center of Neurology and Psychiatry, 4-1-1 Ogawahigashi-Cho Kodaira, Tokyo 187-8502, Japan.

出版信息

Neurol India. 2008 Jul-Sep;56(3):325-32. doi: 10.4103/0028-3886.43451.

Abstract

The term congenital myopathy is applied to muscle disorders presenting with generalized muscle weakness and hypotonia from early infancy with delayed developmental milestones. The congenital myopathies have been classified into various categories based on morphological findings on muscle biopsy. Although the clinical symptoms may seem homogenous, the genetic basis is remarkably variable. This review will focus on myotubular myopathy, centronuclear myopathy, central core disease, and congenital neuromuscular disease with uniform Type 1 fiber, myopathies that are subjects of our ongoing examinations.

摘要

先天性肌病这一术语适用于从婴儿早期就出现全身肌无力和肌张力减退且发育里程碑延迟的肌肉疾病。根据肌肉活检的形态学发现,先天性肌病已被分为不同类别。尽管临床症状可能看似相同,但其遗传基础却显著不同。本综述将聚焦于中央轴空病、核仁中央性肌病、中央核心疾病以及具有均匀1型纤维的先天性神经肌肉疾病,这些都是我们正在研究的肌病。

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验