Yu Tung-Min, Lin Shih-Hua, Ya-Wen Chuang, Wen Mei-Chin, Chen Yi-Hsing, Cheng Chi-Hung, Chen Cheng-Hsu, Chin Chung-Shi, Shu Kuo-Hsiung
Division of Nephrology, Taichung Veterans General Hospital, Taiwan.
Nephrol Dial Transplant. 2009 Feb;24(2):667-9. doi: 10.1093/ndt/gfn600. Epub 2008 Nov 5.
Acquired Bartter-like syndrome, albeit rare, has not been reported to be associated with sarcoidosis. We describe the case of a 32-year-old male patient who presented with progressive muscular weakness of both lower extremities. Profound hypokalaemia associated with renal (K(+)) wasting, bilateral nephrocalcinosis and high plasma renin activity resembled Bartter's syndrome (BS). Both mediastinal lymph node and renal biopsy demonstrated sarcoidosis with non-caseating granuloma. Genetic testing responsible for hereditary BS or Gitelman's syndrome (GS) was negative. Hypokalaemia was well controlled with the administration of spironolactone with oral steroids and KCl. Early recognition and prompt treatment of sarcoidosis-associated Bartter-like syndrome avoids unnecessary complications.
获得性巴特综合征样综合征虽然罕见,但尚未见与结节病相关的报道。我们描述了一例32岁男性患者,其表现为双下肢进行性肌无力。伴有肾(钾离子)丢失、双侧肾钙质沉着症和高血浆肾素活性的严重低钾血症类似于巴特综合征(BS)。纵隔淋巴结活检和肾活检均显示结节病伴非干酪样肉芽肿。对遗传性BS或吉特曼综合征(GS)相关基因检测为阴性。通过给予螺内酯、口服类固醇和氯化钾,低钾血症得到了良好控制。早期识别并及时治疗结节病相关的巴特综合征样综合征可避免不必要的并发症。