Rogers Jack T, Bush Ashley I, Cho Hyan-Hee, Smith Deborah H, Thomson Andrew M, Friedlich Avi L, Lahiri Debomoy K, Leedman Peter J, Huang Xudong, Cahill Catherine M
Department of Psychiatry, Neurochemistry Laboratory, Massachusetts General Hospital, Charlestown, MA 02129, USA.
Biochem Soc Trans. 2008 Dec;36(Pt 6):1282-7. doi: 10.1042/BST0361282.
The essential metals iron, zinc and copper deposit near the Abeta (amyloid beta-peptide) plaques in the brain cortex of AD (Alzheimer's disease) patients. Plaque-associated iron and zinc are in neurotoxic excess at 1 mM concentrations. APP (amyloid precursor protein) is a single transmembrane metalloprotein cleaved to generate the 40-42-amino-acid Abetas, which exhibit metal-catalysed neurotoxicity. In health, ubiquitous APP is cleaved in a non-amyloidogenic pathway within its Abeta domain to release the neuroprotective APP ectodomain, APP(s). To adapt and counteract metal-catalysed oxidative stress, as during reperfusion from stroke, iron and cytokines induce the translation of both APP and ferritin (an iron storage protein) by similar mechanisms. We reported that APP was regulated at the translational level by active IL (interleukin)-1 (IL-1-responsive acute box) and IRE (iron-responsive element) RNA stem-loops in the 5' untranslated region of APP mRNA. The APP IRE is homologous with the canonical IRE RNA stem-loop that binds the iron regulatory proteins (IRP1 and IRP2) to control intracellular iron homoeostasis by modulating ferritin mRNA translation and transferrin receptor mRNA stability. The APP IRE interacts with IRP1 (cytoplasmic cis-aconitase), whereas the canonical H-ferritin IRE RNA stem-loop binds to IRP2 in neural cell lines, and in human brain cortex tissue and in human blood lysates. The same constellation of RNA-binding proteins [IRP1/IRP2/poly(C) binding protein] control ferritin and APP translation with implications for the biology of metals in AD.
必需金属铁、锌和铜沉积在阿尔茨海默病(AD)患者大脑皮层的β淀粉样肽(Aβ)斑块附近。与斑块相关的铁和锌在浓度为1 mM时具有神经毒性。淀粉样前体蛋白(APP)是一种单跨膜金属蛋白,经切割可产生40 - 42个氨基酸的Aβ肽,这些肽表现出金属催化的神经毒性。在健康状态下,普遍存在的APP在其Aβ结构域内通过非淀粉样生成途径被切割,以释放具有神经保护作用的APP胞外结构域APP(s)。为了适应和对抗金属催化的氧化应激,如在中风再灌注期间,铁和细胞因子通过类似机制诱导APP和铁蛋白(一种铁储存蛋白)的翻译。我们报道APP在翻译水平上受APP mRNA 5'非翻译区中活性白细胞介素-1(IL-1,IL-1反应性急性框)和铁反应元件(IRE)RNA茎环的调节。APP的IRE与经典的IRE RNA茎环同源,后者结合铁调节蛋白(IRP1和IRP2),通过调节铁蛋白mRNA翻译和转铁蛋白受体mRNA稳定性来控制细胞内铁稳态。APP的IRE与IRP1(细胞质顺乌头酸酶)相互作用,而经典的H-铁蛋白IRE RNA茎环在神经细胞系、人脑皮层组织和人血液裂解物中与IRP2结合。相同的RNA结合蛋白组合(IRP1/IRP2/聚(C)结合蛋白)控制铁蛋白和APP的翻译,这对AD中金属的生物学特性具有重要意义。