Suresh Chandra Sekharan, Ali Aiman A
Department of Biomedical Dental Sciences, College of Dentistry, King Faisal University, Saudi Arabia.
Med Oral Patol Oral Cir Bucal. 2008 Dec 1;13(12):E761-4.
Desmoid tumors are rare neoplasms accounting for 0.03% of all neoplasms and have an estimated incidence of 2 to 4 per million per year. World Health Organization currently refers to all of the deep types of fibromatosis as desmoid-type of fibromatoses. The term "desmoid" refers to the hard, tendon-like appearance of the tumor. The etiological factors suggested include genetic, endocrine and physical factors. About fifty percent of desmoid tumors arise in the abdominal region. The extra-abdominal desmoid tumors present a difficult problem in recognition and management especially because of the striking discrepancy between its deceptively harmless microscopic appearance and its potential to attain a large size, to recur, and to infiltrate neighboring tissues in the manner of a fibrosarcoma. Desmoid tumors are very rare in the oral cavity with less than 5% of cases constituting oral soft tissue fibromatosis. A 22-year old mentally retarded female patient with desmoid tumor occurring in the tongue is presented here.
硬纤维瘤是罕见肿瘤，占所有肿瘤的0.03%，估计年发病率为每百万人口2至4例。世界卫生组织目前将所有深部纤维瘤病类型归类为硬纤维瘤型纤维瘤病。“硬纤维瘤”一词指的是肿瘤坚硬、类似肌腱的外观。推测的病因包括遗传、内分泌和物理因素。约50%的硬纤维瘤发生于腹部区域。腹外硬纤维瘤在识别和处理方面存在难题，特别是因为其显微镜下看似无害的外观与其可能长得很大、复发以及以纤维肉瘤的方式浸润邻近组织之间存在明显差异。硬纤维瘤在口腔非常罕见，占口腔软组织纤维瘤病病例不到5%。本文报告一名22岁患有舌部硬纤维瘤的智障女性患者。
