Damjanović Miodrag R, Dordević-Radojković Danijela, Perisić Zoran, Apostolović Svetlana, Koraćević Goran, Pavlović Milan, Tomasević Miloje, Janković Ruzica
Klinicki centar, Klinika za kardiovaskularne bolesti, Nis.
Vojnosanit Pregl. 2008 Nov;65(11):847-50. doi: 10.2298/vsp0811847d.
Ebstein's anomaly is characterized by a displacement of the tricuspid valve toward apex, because of anomalous attachment of the tricuspid leaflets. There are type B of Wolff-Parkinson-White (WPW) syndrome and paroxysmal arrhythmias in more than a half of all patients.
We presented a female, 32-year old, with frequent paroxysms of atrial fibrillation. After conversion of rhythm an ECG showed WPW syndrome. Echocardiographic examination discovered normal size of the left cardiac chambers with paradoxical ventricular septal motion. The right ventricle was very small because of its atrialization. The origin of the tricuspid valve was 20 mm closer to apex of the right ventricle than the origin of the mitral valve. Electrophysiological examination showed a posterolateral right accesorial pathway. Atrial fibrillation was induced very easily in electrophysiological laboratory and a successful ablation of accessorial pathway was made. There were no WPW syndrome and paroxysms of atrial fibrillation after that.
Ebstein's anomaly is one of the reasons of paroxysmal atrial fibrillation, especially in young persons with WPW syndrome.
埃布斯坦畸形的特征是三尖瓣叶附着异常，导致三尖瓣向心尖移位。超过半数的患者存在B型预激综合征（WPW）和阵发性心律失常。
我们报告了一名32岁女性，频繁发作心房颤动。心律转复后心电图显示WPW综合征。超声心动图检查发现左心腔大小正常，室间隔运动反常。右心室因心房化而非常小。三尖瓣起源比二尖瓣起源距右心室心尖近20毫米。电生理检查显示后外侧右附加旁路。在电生理实验室很容易诱发心房颤动，并成功消融了附加旁路。此后未再出现WPW综合征和心房颤动发作。
埃布斯坦畸形是阵发性心房颤动的原因之一，尤其是在患有WPW综合征的年轻人中。
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