Dartnell Jo, Pilling John, Ferner Rosalie, Cane Paul, Lang-Lazdunski Loïc
Department of Thoracic Surgery, Guy's and St Thomas' Hospitals NHS Trust, London, United Kingdom.
J Thorac Oncol. 2009 Jan;4(1):135-7. doi: 10.1097/JTO.0b013e31819151ab.
Malignant triton tumor is a divergent malignant peripheral nerve sheath tumor with rhabdomyoblastic differentiation. We report a case of malignant triton tumor arising in the brachial plexus of a 28-year-old women with neurofibromatosis type 1. Fluorodeoxyglucose-positron emission tomography-computed tomography before excision demonstrated a tumor with a maximum standard uptake value of 21 at 4 hours postinjection. The patient underwent complete excision of the tumor through median sternotomy and left supraclavicular approach. Adjuvant radiotherapy and chemotherapy were planned but the patient died of metastatic disease within 3 months of surgical resection.
恶性蝾螈瘤是一种具有横纹肌母细胞分化的异质性恶性外周神经鞘瘤。我们报告一例发生于一名1型神经纤维瘤病的28岁女性臂丛神经的恶性蝾螈瘤。切除术前的氟脱氧葡萄糖正电子发射断层扫描-计算机断层扫描显示，注射后4小时肿瘤的最大标准摄取值为21。患者通过正中胸骨切开术和左锁骨上入路接受了肿瘤的完整切除。计划进行辅助放疗和化疗，但患者在手术切除后3个月内死于转移性疾病。
