García Román J M, Bañares Cañizares R, García Castaño J, Santos Castro L, Clemente Ricote G
Servicio de Medicina Interna I, Hospital General Gregorio Marañón, Madrid.
An Med Interna. 1991 Jan;8(1):27-9.
The case of a 57-year-old male diagnosed as having Budd-Chiari syndrome secondary to a polycythemia vera, which produced a thrombosis of the suprahepatic veins as a first manifestation, is presented. The rarity of this clinical case and the rapidly lethal evolution of the patient, confirms the bad prognosis of this association.
本文报告了一例57岁男性患者,诊断为真性红细胞增多症继发布加综合征,其首发表现为肝上静脉血栓形成。该临床病例的罕见性以及患者迅速致命的病程,证实了这种关联的不良预后。