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Liver disease in infancy: a 20 year perspective.

作者信息

Mieli-Vergani G, Howard E R, Mowat A P

机构信息

Department of Child Health, King's College School of Medicine and Dentistry, London.

出版信息

Gut. 1991 Sep;Suppl(Suppl):S123-8. doi: 10.1136/gut.32.suppl.s123.

DOI:10.1136/gut.32.suppl.s123
PMID:1916464
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1405223/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6c12/1405223/facf1a18526c/gut00594-0127-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6c12/1405223/7e713948cb4b/gut00594-0126-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6c12/1405223/facf1a18526c/gut00594-0127-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6c12/1405223/7e713948cb4b/gut00594-0126-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/6c12/1405223/facf1a18526c/gut00594-0127-a.jpg

相似文献

1
Liver disease in infancy: a 20 year perspective.婴儿期肝病：20年回顾
Gut. 1991 Sep;Suppl(Suppl):S123-8. doi: 10.1136/gut.32.suppl.s123.
2
Portoenterostomy in a case of Alagille's syndrome with extrahepatic biliary atresia.针对一例伴有肝外胆管闭锁的阿拉吉耶综合征患者进行的门肠吻合术。
J Pediatr Surg. 1991 Jan;26(1):111-3. doi: 10.1016/0022-3468(91)90445-y.
3
Hepatolithiasis after hepatic portoenterostomy for biliary atresia.先天性胆管闭锁肝门空肠吻合术后肝内胆管结石
J Pediatr Surg. 2006 Apr;41(4):808-11. doi: 10.1016/j.jpedsurg.2005.12.036.
4
SZ phenotype alpha-1-antitrypsin deficiency with paucity of the interlobular bile ducts.伴有小叶间胆管稀少的α-1抗胰蛋白酶缺乏症的SZ表型
Aust Paediatr J. 1987 Feb;23(1):55-6. doi: 10.1111/j.1440-1754.1987.tb02177.x.
5
Kasai portoenterostomy--new insights from hepatic morphology.肝门空肠吻合术——肝脏形态学的新见解
J Pediatr Surg. 2005 Feb;40(2):322-6. doi: 10.1016/j.jpedsurg.2004.10.018.
6
Hepatic calcification in an anicteric patient with biliary atresia after hepatic portoenterostomy.肝门空肠吻合术后无黄疸的胆道闭锁患者出现肝钙化。
Acta Paediatr Jpn. 1994 Jun;36(3):294-6. doi: 10.1111/j.1442-200x.1994.tb03184.x.
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Intrahepatic cystic lesions after hepatic portoenterostomy for biliary atresia with bile lake and dilated bile ducts.肝门空肠吻合术后肝内囊性病变，伴胆汁湖和胆管扩张，用于治疗胆道闭锁。
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Biliary atresia.胆道闭锁
Semin Pediatr Surg. 1992 May;1(2):115-24.
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Histopathologic approach to metabolic liver disease: Part 1.
Pediatr Dev Pathol. 1998 May-Jun;1(3):179-99. doi: 10.1007/s100249900026.
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Intrahepatic biliary cysts presenting before hepatic portoenterostomy in biliary atresia.肝内胆管囊肿在胆道闭锁患者肝门空肠吻合术前出现。
J Pediatr Gastroenterol Nutr. 2006 Apr;42(4):440-2. doi: 10.1097/01.mpg.0000189352.63290.0a.

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Hepatocellular carcinoma as a complication of Niemann-Pick disease type C1.尼曼-匹克病 C1 型合并肝细胞癌 1 例
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Neonatal Cholestasis Over Time: Changes in Epidemiology and Outcome in a Cohort of 154 Patients From a Portuguese Tertiary Center.新生儿胆汁淤积症随时间变化：来自葡萄牙一家三级医疗中心的154例患者队列的流行病学及预后变化

本文引用的文献

1
Outcome of liver disease associated with alpha 1 antitrypsin deficiency (PiZ). Implications for genetic counselling and antenatal diagnosis.与α1抗胰蛋白酶缺乏症（PiZ）相关的肝脏疾病的转归。对遗传咨询和产前诊断的意义。
Arch Dis Child. 1983 Nov;58(11):882-7. doi: 10.1136/adc.58.11.882.
2
Early assessment of evolution of liver disease associated with alpha 1-antitrypsin deficiency in childhood.儿童α1-抗胰蛋白酶缺乏症相关肝病演变的早期评估。
J Pediatr. 1983 May;102(5):661-5. doi: 10.1016/s0022-3476(83)80230-3.
3
Biliary atresia and other structural anomalies in the congenital polysplenia syndrome.
Front Pediatr. 2020 Jun 30;8:351. doi: 10.3389/fped.2020.00351. eCollection 2020.
4
Niemann-Pick disease type C in the newborn period: a single-center experience.尼曼-匹克病 C 型在新生儿期：单中心经验。
Eur J Pediatr. 2017 Dec;176(12):1669-1676. doi: 10.1007/s00431-017-3020-y. Epub 2017 Sep 27.
5
Early Diagnosis of Spectrum Liver Disorders by Next Generation Sequencing.通过下一代测序技术对肝脏疾病谱进行早期诊断
Pediatr Gastroenterol Hepatol Nutr. 2017 Jun;20(2):114-123. doi: 10.5223/pghn.2017.20.2.114. Epub 2017 Jun 28.
6
Observational cohort study of the natural history of Niemann-Pick disease type C in the UK: a 5-year update from the UK clinical database.英国尼曼-匹克病C型自然病史的观察性队列研究：来自英国临床数据库的5年更新
BMC Neurol. 2015 Dec 15;15:257. doi: 10.1186/s12883-015-0511-1.
7
Diagnostic value of procalcitonin and apo-e in extrahepatic biliary atresia.降钙素原和载脂蛋白E在肝外胆道闭锁中的诊断价值
Iran J Pediatr. 2014 Oct;24(5):623-9. Epub 2014 Feb 18.
8
Diversity of disorders causing neonatal cholestasis - the experience of a tertiary pediatric center in Germany.导致新生儿胆汁淤积症的疾病多样性 - 德国一家三级儿科中心的经验。
Front Pediatr. 2014 Jun 23;2:65. doi: 10.3389/fped.2014.00065. eCollection 2014.
9
The role of decreased levels of Niemann-Pick C1 intracellular cholesterol transport on obesity is reversed in the C57BL/6J, metabolic syndrome mouse strain: a metabolic or an inflammatory effect?Niemann-Pick C1 细胞内胆固醇转运水平降低在肥胖中的作用在 C57BL/6J，代谢综合征小鼠品系中被逆转：是代谢作用还是炎症作用？
J Appl Genet. 2012 Aug;53(3):323-30. doi: 10.1007/s13353-012-0099-8. Epub 2012 May 15.
10
Genetic variation in the mouse model of Niemann Pick C1 affects female, as well as male, adiposity, and hepatic bile transporters but has indeterminate effects on caveolae.尼曼匹克 C1 型小鼠模型中的遗传变异影响雌性和雄性肥胖，以及肝胆汁转运体，但对小窝有不确定的影响。
Gene. 2012 Jan 10;491(2):128-34. doi: 10.1016/j.gene.2011.10.010. Epub 2011 Oct 14.
先天性多脾综合征中的胆道闭锁及其他结构异常。
J Pediatr. 1974 Nov;85(5):649-55. doi: 10.1016/s0022-3476(74)80508-1.
4
Results of surgical treatment for extrahepatic biliary atresia in United Kingdom 1980-2. Survey conducted on behalf of the British Paediatric Association Gastroenterology Group and the British Association of Paediatric Surgeons.1980 - 1982年英国肝外胆道闭锁的外科治疗结果。代表英国儿科学会胃肠病学组和英国儿科学会外科医生协会进行的调查。
Br Med J (Clin Res Ed). 1985 Feb 2;290(6465):345-7. doi: 10.1136/bmj.290.6465.345.
5
Syndromic paucity of interlobular bile ducts (Alagille syndrome or arteriohepatic dysplasia): review of 80 cases.综合征性小叶间胆管稀少（阿拉吉耶综合征或动脉性肝发育不良）：80例病例回顾
J Pediatr. 1987 Feb;110(2):195-200. doi: 10.1016/s0022-3476(87)80153-1.
6
Syndromic paucity of the intrahepatic bile ducts: diagnostic difficulty; severe morbidity throughout early childhood.综合征性肝内胆管稀少：诊断困难；幼儿期发病率高。
J Pediatr Gastroenterol Nutr. 1987 Nov-Dec;6(6):865-71. doi: 10.1097/00005176-198711000-00008.
7
Bacterial cholangitis after surgery for biliary atresia.胆道闭锁手术后的细菌性胆管炎。
J Pediatr. 1987 Dec;111(6 Pt 1):824-9. doi: 10.1016/s0022-3476(87)80195-6.
8
alpha 1-Antitrypsin: molecular pathology, leukocytes, and tissue damage.α1-抗胰蛋白酶：分子病理学、白细胞与组织损伤
J Clin Invest. 1986 Dec;78(6):1427-31. doi: 10.1172/JCI112731.
9
Prenatal diagnosis of alpha-1-antitrypsin deficiency by fetal blood sampling.通过胎儿血样采集对α-1-抗胰蛋白酶缺乏症进行产前诊断。
Prenat Diagn. 1987 Feb;7(2):101-8. doi: 10.1002/pd.1970070206.
10
Primary sclerosing cholangitis in childhood.儿童原发性硬化性胆管炎
Gastroenterology. 1987 May;92(5 Pt 1):1226-35. doi: 10.1016/s0016-5085(87)91082-1.