Kelly Alice, Pomarico Luciana, de Souza Ivete Pomarico Ribeiro
Department of Pediatric Dentistry and Orthodontics, School of Dentistry, Federal University of Rio de Janeiro, Brazil.
Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2009 May;107(5):673-7. doi: 10.1016/j.tripleo.2008.11.017. Epub 2009 Feb 8.
Idiopathic hypoparathyroidism is a rare endocrinopathy whose origin is unknown, and which is characterized by a deficiency of parathyroid hormone causing low serum calcium and high serum phosphorus concentrations. Disorders of ectodermal tissues are common in this pathology, and enamel hypoplasia is the most frequently found dental pathology. This article describes the case of a 9-year-old child with hypoparathyroidism that had gone undiagnosed for 6 years. The permanent dentition showed enamel hypoplasia, delayed eruption, and cessation of root formation (i.e., shortened roots), resulting from nontreated hypocalcemia during the developmental phase of the dentition.
特发性甲状旁腺功能减退症是一种罕见的内分泌病，病因不明，其特征是甲状旁腺激素缺乏导致血清钙浓度降低和血清磷浓度升高。外胚层组织紊乱在这种病理情况下很常见，釉质发育不全是最常见的牙齿病理表现。本文描述了一名9岁甲状旁腺功能减退症患儿的病例，该患儿6年来一直未被诊断出来。恒牙列出现釉质发育不全、萌出延迟和牙根形成停止（即牙根缩短），这是由于牙列发育阶段未治疗的低钙血症所致。
