Billoo Abdul Gaffar, Lone Saira Waqar, Siddiqui Salman, Atiq Huba
Department of Pediatrics, The Aga Khan University Hospital, Karachi.
J Pak Med Assoc. 2009 Jan;59(1):42-3.
Kawasaki disease, also known as mucocutaneous lymph node syndrome or infantile polyarteritis nodosa is an acute febrile vasculitis of unknown etiology with a predilection for coronary arteries and potential for aneurysm formation. In Incomplete Kawasaki disease, children with fever lack the sufficient number of criteria to fulfill the epidemiologic case definition and are diagnosed when coronary artery disease is detected. We present a case report of a one and a half years old girl who came with features of incomplete Kawasaki disease, high grade fever, irritability, history of conjunctivitis and cracking of lips. She was investigated and had a platelet count of 902 x 10(9)/L, ESR was 71 mm/hr and CRP was also raised to 12.8 mg/l. Cardiac evaluation and echocardiography was done which showed dilated coronary arteries >3mm on the left side and 4mm on the right side with early aneurysmal changes. She was treated with immunoglobulin and aspirin and improved.
川崎病，又称皮肤黏膜淋巴结综合征或小儿结节性多动脉炎，是一种病因不明的急性发热性血管炎，易累及冠状动脉且有形成动脉瘤的可能。在不完全川崎病中，发热儿童缺乏足够数量的符合流行病学病例定义的标准，在检测到冠状动脉疾病时才被诊断。我们报告一例1岁半女童，其表现为不完全川崎病，高热、烦躁、有结膜炎病史及嘴唇干裂。对她进行了检查，血小板计数为902×10⁹/L，血沉为71mm/小时，C反应蛋白也升至12.8mg/L。进行了心脏评估和超声心动图检查，结果显示左侧冠状动脉扩张>3mm，右侧为4mm，并伴有早期动脉瘤样改变。她接受了免疫球蛋白和阿司匹林治疗后病情好转。
