Ozerkan Filiz, Güngör Hasan, Zoghi Mehdi, Nalbantgil Sanem
Ege Universitesi Tip Fakültesi, Kardiyoloji Anabilim Dali, Izmir, Turkey.
Turk Kardiyol Dern Ars. 2009 Jan;37(1):53-6.
Hypocalcemic cardiomyopathy due to hypoparathyroidism is a very rare condition. Ensuing heart failure due to hypocalcemia is refractory to conventional treatment. We reported a 41-year-old man who developed cardiac failure due to hypocalcemia secondary to idiopathic hypoparathyroidism. Echocardiography showed biventricular low ejection fraction, dilated heart chambers, pulmonary hypertension, and valvular regurgitations. Serum calcium and parathyroid hormone levels were low. After treatment of heart failure and calcium-vitamin D supplementation, signs and symptoms of heart failure improved rapidly. At 6 months, biventricular systolic and diastolic functions returned to normal. Serum calcium level should be monitored in every patient with cardiac failure and hypocalcemia should be considered in patients with refractory heart failure.
甲状旁腺功能减退所致的低钙血症性心肌病是一种非常罕见的病症。由低钙血症引发的心力衰竭对传统治疗无效。我们报告了一名41岁男性,他因特发性甲状旁腺功能减退继发低钙血症而出现心力衰竭。超声心动图显示双心室射血分数降低、心腔扩大、肺动脉高压和瓣膜反流。血清钙和甲状旁腺激素水平较低。在心力衰竭治疗及补充钙和维生素D后,心力衰竭的体征和症状迅速改善。6个月时,双心室收缩和舒张功能恢复正常。对于每一位心力衰竭患者都应监测血清钙水平,对于难治性心力衰竭患者应考虑低钙血症的可能。