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完全性宫颈和部分性阴道发育不全情况下的子宫水平扭转:一例报告

Horizontal uterine torsion in the setting of complete cervical and partial vaginal agenesis: a case report.

作者信息

Omurtag Kenan, Session Donna, Brahma Pavna, Matlack Angela, Roberts Carla

机构信息

Department of Gynecology and Obstetrics, Emory University School of Medicine, Atlanta, Georgia, USA.

出版信息

Fertil Steril. 2009 May;91(5):1957.e13-5. doi: 10.1016/j.fertnstert.2009.01.058. Epub 2009 Feb 24.

Abstract

OBJECTIVE

To report a case in which uterine torsion in a nulligravid female adolescent was noted upon surgical management of complete cervical and partial vaginal agenesis.

DESIGN

Case report.

SETTING

University hospital.

PATIENT(S): A 13-year-old nulligravid adolescent female.

INTERVENTION(S): Ultrasound-guided vaginal exploration, diagnostic laparoscopy, and hysterectomy.

MAIN OUTCOME MEASURE(S): Uterine torsion as complication of cervical agenesis and its management.

RESULT(S): Complete cervical agenesis, hematometra, and resultant 180-degree horizontal uterine torsion and sacral entrapment.

CONCLUSION(S): Cervical agenesis can be a risk factor for uterine torsion. Hysterectomy is a common treatment due to resultant hematometra, pelvic pain, and severe endometriosis, although rare case reports show success with uterovaginal recanalization in cases with cervical dysgenesis.

摘要

目的

报告一例在对完全性宫颈和部分阴道发育不全进行手术治疗时发现未孕青春期女性子宫扭转的病例。

设计

病例报告。

地点

大学医院。

患者

一名13岁未孕青春期女性。

干预措施

超声引导下阴道探查、诊断性腹腔镜检查及子宫切除术。

主要观察指标

子宫扭转作为宫颈发育不全的并发症及其处理。

结果

完全性宫颈发育不全、子宫积血,导致180度水平子宫扭转及骶骨嵌顿。

结论

宫颈发育不全可能是子宫扭转的一个危险因素。由于出现子宫积血、盆腔疼痛和严重子宫内膜异位症,子宫切除术是常见的治疗方法,尽管罕见病例报告显示宫颈发育异常病例中行子宫阴道再通术取得成功。

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