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真性红细胞增多症中的巨大脑室内血栓形成。

Massive intraventricular thrombus in polycythemia vera.

作者信息

Yuan Shi-Min, Shinfeld Amihay, Raanani Ehud

机构信息

Department of Cardiac and Thoracic Surgery, The Chaim Sheba Medical Center, Tel Hashomer, Israel.

出版信息

J Card Surg. 2009 Mar-Apr;24(2):110-2. doi: 10.1111/j.1540-8191.2008.00621.x.

Abstract

Polycythemia vera is a chronic myeloproliferative disorder which is prone to thrombotic complications. However, thrombosis of the cardiovascular system is an extremely rare complication of polycythemia vera. We describe a 76-year-old male patient who developed congestive heart failure due to massive intraventricular thrombus with pulmonary valvular involvement. Surgical treatment under cardiopulmonary bypass proved to be the sole solution for such a condition.

摘要

真性红细胞增多症是一种慢性骨髓增殖性疾病,易发生血栓并发症。然而,心血管系统血栓形成是真性红细胞增多症极为罕见的并发症。我们描述了一名76岁男性患者,他因巨大的心室内血栓累及肺动脉瓣而发生充血性心力衰竭。体外循环下的手术治疗被证明是治疗这种情况的唯一方法。

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