Soni-Jaiswal A, Woolford T J
Department of Otolaryngology, Manchester Royal Infirmary, UK.
J Laryngol Otol. 2009 Jun;123(6):695-6. doi: 10.1017/S0022215109004964. Epub 2009 Mar 11.
Most patients with hereditary haemorrhagic telangiectasia suffer with frequent episodes of epistaxis. The aim of this case report is to highlight the effect on epistaxis, occurring in hereditary haemorrhagic telangiectasia, when nasal airflow ceases.
We present the interesting case of a patient with hereditary haemorrhagic telangiectasia who experienced cessation of her recurrent, refractory epistaxis through the development of coexisting polyp disease. The patient's enlarged, grade three nasal polyps were behaving as physiological obturators, limiting airflow through her nose. This reduced the intranasal trauma and subsequent frequency of her nosebleeds.
Epistaxis is a debilitating part of hereditary haemorrhagic telangiectasia, and poses a frequent management challenge. Our patient was more tolerant of her grade three nasal polyps than of her recurrent epistaxis. This case highlights the importance of reducing nasal airflow when treating patients with hereditary haemorrhagic telangiectasia.
大多数遗传性出血性毛细血管扩张症患者经常鼻出血。本病例报告的目的是强调当鼻气流停止时,对遗传性出血性毛细血管扩张症患者鼻出血的影响。
我们呈现了一例有趣的遗传性出血性毛细血管扩张症患者,其复发性难治性鼻出血因并发鼻息肉病而停止。患者肿大的三级鼻息肉起到了生理性填塞物的作用,限制了通过鼻腔的气流。这减少了鼻内创伤及随后鼻出血的频率。
鼻出血是遗传性出血性毛细血管扩张症中使人衰弱的一部分,并且经常带来治疗挑战。我们的患者对三级鼻息肉的耐受性高于对复发性鼻出血的耐受性。本病例强调了在治疗遗传性出血性毛细血管扩张症患者时减少鼻气流的重要性。