Obstructing leiomyoma of the common hepatic duct bifurcation simulating a Klatskin tumor.

The first reported case of a leiomyoma of the proximal bile duct simulating a Klatskin tumor and causing obstructive cholestasis is presented. Diagnosis was made at the time of exploratory surgery. Surgical management included complete excision with Roux-en-Y hepatic-ojejunostomy.