Modi Amit, Lipnevicius Arturas, Moorjani Narain, Haw Marcus
Wessex Cardiothoracic Centre, Southampton University Hospitals NHS Trust, Southampton, UK.
Interact Cardiovasc Thorac Surg. 2009 Jun;8(6):703-4. doi: 10.1510/icvts.2009.203562. Epub 2009 Mar 20.
Primary spindle cell sarcoma of the left atrium is a rare tumour. Optimal treatment is to obtain complete surgical clearance of the tumour. The anatomic location of the tumour, infiltration into vital structures and difficult access provides a surgical challenge for resection of the lesion and reconstruction of the defect. The prognosis of patients with a primary cardiac sarcoma is very poor because of their resistance to treatment with chemotherapy and radiotherapy. Metastases and local recurrences are common despite optimal multimodality treatment. This report describes a 48-year-old gentleman who underwent multiple surgeries to achieve an 11-year survival since the diagnosis. The operative techniques have been described.
左心房原发性梭形细胞肉瘤是一种罕见肿瘤。最佳治疗方法是手术完全切除肿瘤。肿瘤的解剖位置、浸润至重要结构以及手术入路困难,给病变切除及缺损修复带来了手术挑战。原发性心脏肉瘤患者的预后很差,因为他们对化疗和放疗耐药。尽管采取了最佳的多模式治疗,转移和局部复发仍很常见。本报告描述了一名48岁男性,自诊断以来接受了多次手术,存活了11年。文中描述了手术技术。