Wang Xiaoling, Chinnam Meenalakshmi, Wang Jianmin, Wang Yanqing, Zhang Xiaojing, Marcon Edyta, Moens Peter, Goodrich David W
Department of Pharmacology & Therapeutics, Roswell Park Cancer Institute, Elm & Carlton Streets, Buffalo, NY 14263, USA.
Mol Cell Biol. 2009 May;29(10):2794-803. doi: 10.1128/MCB.01633-08. Epub 2009 Mar 23.
Accumulating evidence suggests that regulation of RNA processing through an RNP-driven mechanism is important for coordinated gene expression. This hypothesis predicts that defects in RNP biogenesis will adversely affect the elaboration of specific gene expression programs. To explore the role of RNP biogenesis on mammalian development, we have characterized the phenotype of mice hypomorphic for Thoc1. Thoc1 encodes an essential component of the evolutionarily conserved TREX complex. TREX accompanies the elongating RNA polymerase II and facilitates RNP assembly and recruitment of RNA processing factors. Hypomorphic Thoc1 mice are viable despite significantly reduced Thoc1 expression in the tissues examined. While most tissues of Thoc1-deficient mice appear to develop and function normally, gametogenesis is severely compromised. Male infertility is associated with a loss in spermatocyte viability and abnormal endocrine signaling. We suggest that loss of spermatocyte viability is a consequence of defects in the expression of genes required for normal differentiation of cell types within the testes. A number of the genes affected appear to be direct targets for regulation by Thoc1. These findings support the notion that Thoc1-mediated RNP assembly contributes to the coordinated expression of genes necessary for normal differentiation and development in vivo.
越来越多的证据表明,通过核糖核蛋白(RNP)驱动机制对RNA加工进行调控对于协调基因表达很重要。这一假说预测,RNP生物合成中的缺陷将对特定基因表达程序的精细调控产生不利影响。为了探究RNP生物合成在哺乳动物发育中的作用,我们对Thoc1基因低表达的小鼠的表型进行了表征。Thoc1编码进化上保守的TREX复合物的一个必需组分。TREX伴随延伸中的RNA聚合酶II,并促进RNP组装以及RNA加工因子的募集。尽管在所检测的组织中Thoc1表达显著降低,但Thoc1基因低表达的小鼠仍可存活。虽然Thoc1缺陷小鼠的大多数组织似乎发育和功能正常,但配子发生受到严重损害。雄性不育与精母细胞活力丧失和异常内分泌信号传导有关。我们认为,精母细胞活力丧失是睾丸内正常细胞类型分化所需基因表达缺陷的结果。许多受影响的基因似乎是Thoc1调控的直接靶点。这些发现支持了这样一种观点,即Thoc1介导的RNP组装有助于体内正常分化和发育所需基因的协调表达。