挽救性自身免疫性血友病
Autoimmune hemophilia at rescue.
作者信息
Mannucci Pier Mannuccio, Peyvandi Flora
机构信息
Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Department of Medicine and Medical Specialities, University of Milan, IRCCS Maggiore Hospital, Mangiagalli and Regina Elena Foundation, Italy.
出版信息
Haematologica. 2009 Apr;94(4):459-61. doi: 10.3324/haematol.2009.005777.
Abstract
Acquired hemophilia is much more clinically severe than congenital hemophilia, and is more difficult to diagnose, also because cases are seen in an array of clinical settings that are not usually equipped to tackle them. In this perspective article Drs. Mannucci and Peyvandi examine the management of this condition. See related article on page 566.
摘要
获得性血友病在临床上比先天性血友病严重得多，且更难诊断，这也是因为该病病例出现在一系列通常没有应对能力的临床环境中。在这篇观点文章中，曼努奇医生和佩万迪医生探讨了这种疾病的治疗方法。见第566页的相关文章。
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Autoimmune hemophilia at rescue.挽救性自身免疫性血友病
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Ann N Y Acad Sci. 1991;614:97-105. doi: 10.1111/j.1749-6632.1991.tb43695.x.
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本文引用的文献
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International recommendations on the diagnosis and treatment of patients with acquired hemophilia A.获得性血友病A患者诊断和治疗的国际建议。
Haematologica. 2009 Apr;94(4):566-75. doi: 10.3324/haematol.2008.001743.
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Autoimmune haemophilia.自身免疫性血友病
Blood Transfus. 2008 Jan;6(1):6-7. doi: 10.2450/2008.0004-08.
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Acquired factor VIII inhibitors.获得性凝血因子 VIII 抑制剂
Blood. 2008 Jul 15;112(2):250-5. doi: 10.1182/blood-2008-03-143586. Epub 2008 May 7.
4
Acquired hemophilia A in the United Kingdom: a 2-year national surveillance study by the United Kingdom Haemophilia Centre Doctors' Organisation.英国获得性血友病A：英国血友病中心医生组织进行的一项为期两年的全国性监测研究。
Blood. 2007 Mar 1;109(5):1870-7. doi: 10.1182/blood-2006-06-029850. Epub 2006 Oct 17.
5
6
A prospective randomized trial of high and standard dosages of recombinant factor VIIa for treatment of hemarthroses in hemophiliacs with inhibitors.一项关于高剂量和标准剂量重组凝血因子VIIa治疗血友病伴抑制剂患者关节积血的前瞻性随机试验。
J Thromb Haemost. 2006 Feb;4(2):367-71. doi: 10.1111/j.1538-7836.2006.01772.x.
7
Selective B-cell depletion with rituximab for the treatment of patients with acquired hemophilia.使用利妥昔单抗进行选择性B细胞清除治疗获得性血友病患者。
Blood. 2004 Jun 15;103(12):4424-8. doi: 10.1182/blood-2003-11-4075. Epub 2004 Mar 2.
8
Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura.急性血栓性血小板减少性紫癜中针对血管性血友病因子裂解蛋白酶的抗体。
N Engl J Med. 1998 Nov 26;339(22):1585-94. doi: 10.1056/NEJM199811263392203.
9
von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome.血栓性血小板减少性紫癜和溶血尿毒综合征中的血管性血友病因子裂解蛋白酶
N Engl J Med. 1998 Nov 26;339(22):1578-84. doi: 10.1056/NEJM199811263392202.
10
Brief report: autoimmune protein S deficiency in a boy with severe thromboembolic disease.简短报告：一名患有严重血栓栓塞性疾病男孩的自身免疫性蛋白S缺乏症
N Engl J Med. 1993 Jun 17;328(24):1753-7. doi: 10.1056/NEJM199306173282405.
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