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并发白塞病的弥漫性主动脉炎导致严重主动脉瓣反流。

Diffuse aortitis complicating Behçet's disease leading to severe aortic regurgitation.

作者信息

Tai Y T, Fong P C, Ng W F, Fu K H, Chow W H, Lau C P, Wong W S

机构信息

Department of Medicine, University of Hong Kong.

出版信息

Cardiology. 1991;79(2):156-60. doi: 10.1159/000174874.

DOI:10.1159/000174874
PMID:1933967
Abstract

Cardiovascular complications are uncommon in Behçet's disease, but are frequently the cause of morbidity and mortality. Venous and peripheral arterial involvement have been well documented, but involvement of the proximal aorta has rarely been described. This report details a Chinese patient with Behçet's disease. Diffuse aortitis led to proximal aortic dilatation and severe aortic regurgitation necessitating aortic valve replacement. Histopathology of the aorta revealed features similar to those observed in other systemic diseases with aortic involvement.

摘要

心血管并发症在白塞病中并不常见,但常常是发病和死亡的原因。静脉和外周动脉受累已有充分记载,但近端主动脉受累很少被描述。本报告详细介绍了一名患有白塞病的中国患者。弥漫性主动脉炎导致近端主动脉扩张和严重主动脉反流,需要进行主动脉瓣置换。主动脉的组织病理学显示出与其他累及主动脉的全身性疾病中观察到的特征相似。

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Diffuse aortitis complicating Behçet's disease leading to severe aortic regurgitation.并发白塞病的弥漫性主动脉炎导致严重主动脉瓣反流。
Cardiology. 1991;79(2):156-60. doi: 10.1159/000174874.
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Aortitis with severe aortic regurgitation in Behcet's disease: a case report.白塞病致主动脉炎合并重度主动脉瓣反流 1 例报告
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Valved conduit operation for aortic regurgitation associated with Behçet's disease.用于治疗与白塞病相关的主动脉反流的带瓣管道手术。
Jpn J Thorac Cardiovasc Surg. 2000 Jul;48(7):424-7. doi: 10.1007/BF03218169.