Bagwan Izhar N, Desai Saral, Wotherspoon Andrew, Sheppard Mary N
Department of Histopathology, The Royal Brompton Hospital, London, UK.
Interact Cardiovasc Thorac Surg. 2009 Jul;9(1):127-9. doi: 10.1510/icvts.2009.204628. Epub 2009 Apr 7.
Cardiac lymphomas are rare neoplasms and account for a minor proportion of primary cardiac malignancies. Secondary involvement of the heart and pericardium by systemic lymphoma is well documented, but primary lymphomas of heart and pericardium are extremely rare, accounting for approximately 2% of all primary cardiac tumours. Most cases are diagnosed at autopsy, but nowadays, with modern imaging technologies, early diagnosis and treatment is possible. Here, we present two unique incidental presentations of primary cardiac lymphomas (PCL), one in an atrial myxoma and other involving a valvular homograft and discuss the potential pitfalls and prognosis of this rare entity.
心脏淋巴瘤是罕见的肿瘤,在原发性心脏恶性肿瘤中占比很小。系统性淋巴瘤累及心脏和心包已有充分记录,但心脏和心包的原发性淋巴瘤极为罕见,约占所有原发性心脏肿瘤的2%。大多数病例在尸检时被诊断出来,但如今,借助现代成像技术,早期诊断和治疗成为可能。在此,我们展示原发性心脏淋巴瘤(PCL)的两种独特的偶然表现,一种发生在心房黏液瘤中,另一种累及瓣膜同种异体移植物,并讨论这种罕见疾病的潜在陷阱和预后。