Garganese Maria C, De Sio Luigi, Serra Annalisa, De Ioris Maria A, Bock Caterina, Donfrancesco Alberto, Ciofetta Gianclaudio
Nuclear Medicine Unit, Ospedale Pediatrico Bambino Gesù Rome, Italy.
Clin Nucl Med. 2009 Mar;34(3):155-7. doi: 10.1097/RLU.0b013e3181966dfb.
Hypertrophic osteoarthropathy (HOA) is characterized by digital clubbing, long bone periosteal reaction, and polyarthralgias. Primary familial HOA is very rare and is not associated with underlying disorders and has a good prognosis. Secondary pediatric nonneoplastic HOA is associated with cystic fibrosis, congenital heart disease, biliary atresia, and inflammatory bowel disease. Secondary neoplastic HOA may be associated with intra or extrathoracic tumors.A 5-year-old girl was admitted to our hospital for an abdominal mass, digital clubbing, and diffuse articular pain. The bone scan revealed symmetrical tracer uptake in the long bones. Upper and lower extremity x-rays were diagnostic for HOA. Paraneoplastic HOA in childhood accounts for not more than 12% of HOA paitents. HOA has been reported in 2 other cases of rhabdomyosarcoma.
肥厚性骨关节病(HOA)的特征为杵状指、长骨骨膜反应和多关节痛。原发性家族性HOA非常罕见,与潜在疾病无关,预后良好。继发性小儿非肿瘤性HOA与囊性纤维化、先天性心脏病、胆道闭锁和炎症性肠病有关。继发性肿瘤性HOA可能与胸内或胸外肿瘤有关。一名5岁女孩因腹部肿块、杵状指和弥漫性关节疼痛入住我院。骨扫描显示长骨有对称的示踪剂摄取。上肢和下肢X线检查可诊断为HOA。儿童副肿瘤性HOA占HOA患者的比例不超过12%。横纹肌肉瘤的另外2例病例也报告有HOA。