Choi Seok-Keun, Rhee Bong-Arm, Lim Young Jin
Department of Neurosurgery, School of Medicine, Kyung Hee University, Seoul, Korea.
J Korean Neurosurg Soc. 2009 Mar;45(3):196-8. doi: 10.3340/jkns.2009.45.3.196. Epub 2009 Mar 31.
Hemifacial spasm (HFS) is almost always induced by vascular compression but in some cases the cause of HFS are tumors at cerebellopontine angle (CPA) or vascular malformations. We present a rare case of hemifacial spasm caused by epidermoid tumors and the possible pathogenesis of HFS is discussed. A 36-year-old female patient presented with a 27-month history of progressive involuntary facial twitching and had been treated with acupuncture and herb medication. On imaging study, a mass lesion was seen at right CPA. Microvascular decompression combined with mass removal was undertaken through retrosigmoid approach. The lesion was avascular mass and diagnosed with an epidermoid tumor pathologically. Eventually, we found a offending vessel (AICA : anterior inferior cerebellar artery) compressing facial nerve root exit zone (REZ). In case of HFS caused by tumor compression on the facial nerve REZ, surgeons should try to find an offending vessel under the mass. This case supports the vascular compression theory as a pathogenesis of HFS.
面肌痉挛(HFS)几乎总是由血管压迫引起,但在某些情况下,HFS的病因是桥小脑角(CPA)肿瘤或血管畸形。我们报告一例由表皮样肿瘤引起的罕见面肌痉挛病例,并讨论了HFS可能的发病机制。一名36岁女性患者有27个月进行性不自主面部抽搐病史,曾接受针灸和草药治疗。影像学检查发现右侧CPA有一肿块病变。通过乙状窦后入路进行微血管减压联合肿块切除。该病变为无血管肿块,病理诊断为表皮样肿瘤。最终,我们发现一条肇事血管(小脑前下动脉:AICA)压迫面神经根部出口区(REZ)。对于由肿瘤压迫面神经REZ引起的HFS病例,外科医生应尝试在肿块下方找到肇事血管。该病例支持血管压迫理论作为HFS的发病机制。