Ang Estabelle, Pavlos Nathan J, Rea Sarah L, Qi Ming, Chai Tracy, Walsh John P, Ratajczak Thomas, Zheng Ming H, Xu Jiake
Molecular Orthopaedic Laboratory, Centre for Orthopaedic Research, School of Surgery, The University of Western Australia, Nedlands, Western Australia, Australia.
J Cell Physiol. 2009 Aug;220(2):450-9. doi: 10.1002/jcp.21787.
Proteasome inhibitors represent a promising therapy for the treatment of relapsed and/or refractory multiple myeloma, a disease that is concomitant with osteolysis and enhanced osteoclast formation. While blockade of the proteosome pathway has been recently shown to influence osteoclast formation and function, the precise molecular cascade underlying these effects is presently unclear. Here, we provide evidence that proteasome inhibitors directly impair osteoclast formation and function via the disruption of key RANK-mediated signaling cascades. Disruption of the proteosome pathway using selective inhibitors (MG-132, MG-115, and epoxomicin) resulted in the accumulation of p62 and CYLD, and altered the subcellular targeting and distribution of p62 and TRAF6 in osteoclast-like cells. Proteosome inhibition also blocked RANKL-induced NF-kappaB activation, IkappaBalpha degradation and nuclear translocation of p65. The disruption in RANK-signaling correlated dose-dependently with an impairment in osteoclastogenesis, with relative potency epoxomicin > MG-132 > MG-115 based on equimolar concentrations. In addition, these inhibitors were found to impact osteoclastic microtubule organization and attenuate bone resorption. Based on these data we propose that deregulation of key RANK-mediated signaling cascades (p62, TRAF6, CYLD, and IkappaBalpha) underscores proteasome-mediated inhibition of osteolytic bone conditions.
蛋白酶体抑制剂是治疗复发和/或难治性多发性骨髓瘤的一种有前景的疗法,该疾病伴有骨溶解和破骨细胞形成增加。虽然最近已表明阻断蛋白酶体途径会影响破骨细胞的形成和功能,但这些作用背后的确切分子级联反应目前尚不清楚。在此,我们提供证据表明蛋白酶体抑制剂通过破坏关键的RANK介导的信号级联反应直接损害破骨细胞的形成和功能。使用选择性抑制剂(MG-132、MG-115和环氧霉素)破坏蛋白酶体途径导致p62和CYLD积累,并改变了破骨细胞样细胞中p62和TRAF6的亚细胞定位和分布。蛋白酶体抑制还阻断了RANKL诱导的NF-κB激活、IκBα降解和p65的核转位。RANK信号的破坏与破骨细胞生成受损呈剂量依赖性相关,基于等摩尔浓度,相对效力为环氧霉素>MG-132>MG-115。此外,发现这些抑制剂会影响破骨细胞微管组织并减弱骨吸收。基于这些数据我们提出,关键的RANK介导的信号级联反应(p62、TRAF6、CYLD和IκBα)失调是蛋白酶体介导的溶骨性骨疾病抑制的基础。