al-Mulhim I, Sabbah R S, al-Akkad S
Hospital & Research Centre, Riyadh, Kingdom of Saudi Arabia.
Indian J Cancer. 1991 Jun;28(2):53-60.
A retrospective analysis of 21 Saudi children with Histiocytosis-X were reviewed. 13 were males, 8 were females, with a ratio of 1.62:1. Five had unifocal disease while 16 were with multifocal disease. Bone involvement was seen in 19 patients (90.4%), and three patients had organ dysfunction. One patient had family history of Histiocytosis-X. Follow-up was from 1-10 years (Median 3 years). Three patients died, three had recurrences and eight patients had various disabilities (38%). Overall disease free survival was 84.2 percent.
对21例沙特组织细胞增多症-X患儿进行了回顾性分析。13例为男性，8例为女性，男女比例为1.62:1。5例为单病灶疾病，16例为多病灶疾病。19例患者（90.4%）出现骨受累，3例患者出现器官功能障碍。1例患者有组织细胞增多症-X家族史。随访时间为1至10年（中位时间3年）。3例患者死亡，3例复发，8例患者有各种残疾（38%）。总体无病生存率为84.2%。
