Martínez Héctor, Montano Luarde, Rodriguez-Ospina Luis, Campos Zulmari, Muñiz Myrna, Aviles Eric
Cardiology Section, Department of Medicine, Veterans Administration Medical Center of San Juan, Puerto Rico, USA.
Bol Asoc Med P R. 2008 Oct-Dec;100(4):86-8.
Brugada syndrome (BS) is an under recognized condition inherited through autosomal dominant transmission that consists mainly of characteristic electrocardiogram findings with ST segment elevation, in leads V1 through V3, complemented with right bundle-branch block pattern. Patients usually have medical history of prior syncopal episodes and are at risk of sudden cardiac death; although diagnostic studies reveal structurally normal heart. Adequate treatment consists of implantable cardioverter defibrillator which can prevent associated lethal arrhythmias that lead to sudden cardiac death. Correct diagnosis with medical history and characteristic electrocardiographic findings is essential to the physician to prevent unnecessary treatments that can further compromise patient's health status.
Brugada综合征(BS)是一种通过常染色体显性遗传的未被充分认识的疾病,主要表现为V1至V3导联ST段抬高并伴有右束支传导阻滞图形的特征性心电图表现。患者通常有既往晕厥发作史,并有心脏性猝死风险;尽管诊断性检查显示心脏结构正常。充分的治疗包括植入式心脏复律除颤器,其可预防导致心脏性猝死的相关致命性心律失常。通过病史和特征性心电图表现进行正确诊断对医生至关重要,可避免进行可能进一步损害患者健康状况的不必要治疗。