Fakir Ebrahim, Roberts Tina, Stephen Lawrence, Beighton Peter
Faculty of Dentistry, University of the Western Cape, Cape Town, South Africa.
Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2009 Jun;107(6):754-8. doi: 10.1016/j.tripleo.2009.01.037.
Klippel-Trenaunay-Weber syndrome is characterized by a triad of features, namely, vascular nevi, venous varicosities, and hyperplasia of hard and soft tissues in the affected area. Involvement of the orofacial region is uncommon, but nevertheless, a wide range of orofacial abnormalities may necessitate specialized dental and anesthesia management. We have documented the manifestations in 2 affected persons, outlined the nosology, reviewed the literature, and tabulated craniofacial anomalies and orodental complications. Special emphasis is given to the hematologic factors (bleeding tendencies) and vascular involvement (hemangiomata) which may significantly influence orodental management and anesthesia.
克-特-韦综合征的特征为三联征，即血管痣、静脉畸形以及患侧软硬组织增生。口面部受累并不常见，但尽管如此，多种口面部异常可能需要专业的牙科和麻醉处理。我们记录了2例患者的表现，概述了疾病分类学，回顾了文献，并将颅面异常和口腔牙齿并发症制成表格。特别强调了可能显著影响口腔牙齿处理和麻醉的血液学因素（出血倾向）和血管受累情况（血管瘤）。
