Manes J L, Kissane J M, Valdes A J
Cancer. 1977 Jun;39(6):2619-23. doi: 10.1002/1097-0142(197706)39:6<2619::aid-cncr2820390647>3.0.co;2-4.
In reviewing the literature, we found no liver cell carcinoma (LCC) or well-documented adult polycystic kidneys (APK) associated with congenital hepatic fibrosis (CHF). We report a 69-year-old man with CHF, LCC, APK, duplication cyst of distal portion of stomach, two calcified splenic artery aneurysms, myocardial fibrosis and muscular hypertrophy of esophagus. The LCC was grossly predunculated and microscopically showed prominent fibrosis and hyaline intracytoplasmic inclusions in the tumor cells.
在回顾文献时，我们未发现与先天性肝纤维化（CHF）相关的肝细胞癌（LCC）或有充分记录的成人多囊肾（APK）。我们报告一名69岁男性，患有CHF、LCC、APK、胃远端重复囊肿、两个脾动脉钙化动脉瘤、心肌纤维化和食管肌肉肥大。LCC肉眼可见有蒂，显微镜下显示肿瘤细胞中有明显的纤维化和透明细胞质内包涵体。
