Leich Ellen, Salaverria Itziar, Bea Silvia, Zettl Andreas, Wright George, Moreno Victor, Gascoyne Randy D, Chan Wing-Chung, Braziel Rita M, Rimsza Lisa M, Weisenburger Dennis D, Delabie Jan, Jaffe Elaine S, Lister Andrew, Fitzgibbon Jude, Staudt Louis M, Hartmann Elena M, Mueller-Hermelink Hans-Konrad, Campo Elias, Ott German, Rosenwald Andreas
Institute of Pathology, University of Wuerzburg, Josef-Schneider-Strasse 2, Wuerzburg, Germany.
Blood. 2009 Jul 23;114(4):826-34. doi: 10.1182/blood-2009-01-198580. Epub 2009 May 26.
Follicular lymphoma (FL) is genetically characterized by the presence of the t(14;18)(q32;q21) chromosomal translocation in approximately 90% of cases. In contrast to FL carrying the t(14;18), their t(14;18)-negative counterparts are less well studied about their immunohistochemical, genetic, molecular, and clinical features. Within a previously published series of 184 FLs grades 1 to 3A with available gene expression data, we identified 17 FLs lacking the t(14;18). Comparative genomic hybridization and high-resolution single nucleotide polymorphism (SNP) array profiling showed that gains/amplifications of the BCL2 gene locus in 18q were restricted to the t(14;18)-positive FL subgroup. A comparison of gene expression profiles showed an enrichment of germinal center B cell-associated signatures in t(14;18)-positive FL, whereas activated B cell-like, NFkappaB, proliferation, and bystander cell signatures were enriched in t(14;18)-negative FL. These findings were confirmed by immunohistochemistry in an independent validation series of 84 FLs, in which 32% of t(14;18)-negative FLs showed weak or absent CD10 expression and 91% an increased Ki67 proliferation rate. Although overall survival did not differ between FL with and without t(14;18), our findings suggest distinct molecular features of t(14;18)-negative FL.
滤泡性淋巴瘤(FL)的遗传学特征是约90%的病例存在t(14;18)(q32;q21)染色体易位。与携带t(14;18)的FL相比,其t(14;18)阴性的对应物在免疫组织化学、遗传学、分子学和临床特征方面的研究较少。在先前发表的一系列184例1至3A级且有可用基因表达数据的FL中,我们鉴定出17例缺乏t(14;18)的FL。比较基因组杂交和高分辨率单核苷酸多态性(SNP)阵列分析表明,18q上BCL2基因座的增益/扩增仅限于t(14;18)阳性的FL亚组。基因表达谱比较显示,生发中心B细胞相关特征在t(14;18)阳性的FL中富集,而活化B细胞样、NFκB、增殖和旁观者细胞特征在t(14;18)阴性的FL中富集。这些发现通过对84例FL的独立验证系列免疫组织化学得到证实,其中32%的t(14;18)阴性FL显示CD10表达减弱或缺失,91%的Ki67增殖率升高。虽然有或没有t(14;18)的FL的总生存期没有差异,但我们的发现表明t(14;18)阴性的FL具有独特的分子特征。