不完全性卡尼三联征——两例报告
Incomplete Carney triad--a review of two cases.
机构信息
Department of Respiratory Medicine, Aberdeen Royal Infirmary, Foresterhill, Aberdeen, UK AB25 2ZD.
出版信息
QJM. 2009 Sep;102(9):649-53. doi: 10.1093/qjmed/hcp078. Epub 2009 Jun 26.
A curious association of three rare tumours was described by Carney in 1977. 'Carney's triad' characteristically includes multifocal pulmonary chondroma, gastric stromal sarcoma and extra-adrenal paraganglioma. Patients may exhibit complete or incomplete expression of the triad. Carney acknowledged that, of 79 patients, only 17 possessed all three tumours. We report here two patients with incomplete expression of Carney's triad.
1977 年，Carney 描述了三种罕见肿瘤的奇特关联。“Carney 三联征”的特征性表现包括多灶性肺软骨瘤、胃间质肉瘤和肾上腺外副神经节瘤。患者可能表现出三联征的完全或不完全表达。Carney 承认，在 79 名患者中，只有 17 名患者存在所有三种肿瘤。我们在此报告两名不完全表达 Carney 三联征的患者。
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