一名患有2型神经纤维瘤病的儿童的食管丛状神经鞘瘤。

Plexiform schwannoma of the esophagus in a child with neurofibromatosis type 2.

作者信息

Retrosi Giuseppe, Nanni Lorenzo, Ricci Riccardo, Manzoni Carlo, Pintus Claudio

机构信息

Department of Pediatrics, Division of Pediatric Surgery, Università Cattolica del S Cuore, Policlinico A Gemelli, Rome, Italy.

出版信息

J Pediatr Surg. 2009 Jul;44(7):1458-61. doi: 10.1016/j.jpedsurg.2009.03.029.

DOI:10.1016/j.jpedsurg.2009.03.029

PMID:19573680

Abstract

Schwannoma is a benign neoplasia of the peripheral nerve sheath. Its localization in the gastrointestinal tract, and in particular in the esophagus, is very rare. According to the existing literature esophageal schwannoma has been reported so far only in adult patients. We report the case of an 11 year old patient with neurofibromatosis, type 2, who underwent surgical excision of a plexiform schwannoma of the esophagus.

摘要

施万细胞瘤是一种周围神经鞘的良性肿瘤。它在胃肠道，尤其是食管中的定位非常罕见。根据现有文献，迄今为止仅在成年患者中报道过食管施万细胞瘤。我们报告了一例患有2型神经纤维瘤病的11岁患者，该患者接受了食管丛状施万细胞瘤的手术切除。