Halefoğlu Ahmet Mesrur
Department of Radiology, Sişli Etfal Training and Research Hospital, Istanbul, Turkey.
Kulak Burun Bogaz Ihtis Derg. 2007;17(3):171-5.
A 16-year-old male patient complained of right-sided tinnitus and mild deafness of one-month history. He also had a family history of neurofibromatosis type 2 and a history of a prior operation for left vestibular schwannoma a year ago. Otoneurologic examination revealed moderate sensorineural hearing loss. Magnetic resonance imaging demonstrated multiple extra-axial enhancing masses in the vicinity of both hypoglossal nerves, the right vestibular nerve, the left vestibular nerve, the right trigeminal, the left occulomotor, and the right abducens nerves. These findings were evaluated as multiple cranial nerve schwannomas. The case was considered a rare manifestation of neurofibromatosis type 2 without any concomitant abnormality in the central nervous system. Symptomatic medical treatment was initiated and the patient was referred to the neurosurgery department.
一名16岁男性患者主诉右侧耳鸣及轻度耳聋，病程1个月。他有2型神经纤维瘤病家族史，且1年前曾因左侧前庭神经鞘瘤接受手术。耳神经科检查发现中度感音神经性听力损失。磁共振成像显示双侧舌下神经、右侧前庭神经、左侧前庭神经、右侧三叉神经、左侧动眼神经及右侧展神经附近有多个轴外强化肿块。这些表现被评估为多发颅神经鞘瘤。该病例被认为是2型神经纤维瘤病的罕见表现，中枢神经系统无任何伴随异常。开始进行对症治疗，并将患者转诊至神经外科。
