Department of Thoracic Surgery, University of São Paulo School of Medicine Hospital das Clínicas, São Paulo, Brazil.
J Bras Pneumol. 2009 Jun;35(6):515-20. doi: 10.1590/s1806-37132009000600004.
To analyze the outcomes of patients undergoing repair of congenital tracheal stenosis.
This was a retrospective review of congenital tracheal stenosis patients treated between 2001 and 2007 at the University of São Paulo School of Medicine Hospital das Clínicas in São Paulo, Brazil.
Six boys and one girl (age at diagnosis ranging from 28 days to 3 years) were included. Five of the patients also had cardiac or major vessel malformations. The stenosis length was short in three patients, medium in one and long in three. The techniques used were pericardial patch tracheoplasty in three patients, resection and anastomosis in two, slide tracheoplasty in one and vascular ring correction in one. One patient died during surgery due to hypoxia and hemodynamic instability, and one died from septic shock on postoperative day 11. Other complications included pneumonia, arrhythmia, stenosis at the anastomosis level, residual stenosis, granuloma formation and malacia. The mean follow-up period was 31 months; four patients were cured, and one required the use of a T tube to maintain airway patency.
Congenital tracheal stenosis is a curable disease. However, its repair is complex and is associated with high rates of morbidity and mortality.
分析先天性气管狭窄患者的治疗结果。
这是对巴西圣保罗大学医学院附属医院 2001 年至 2007 年期间治疗的先天性气管狭窄患者进行的回顾性研究。
纳入 6 名男孩和 1 名女孩（诊断时年龄为 28 天至 3 岁）。其中 5 例患者还存在心脏或大血管畸形。3 例患者狭窄长度较短，1 例患者狭窄长度中等，3 例患者狭窄长度较长。使用的技术包括 3 例心包片气管成形术、2 例切除和吻合术、1 例滑动气管成形术和 1 例血管环矫正术。1 例患者在手术过程中因缺氧和血流动力学不稳定而死亡，1 例患者在术后第 11 天死于感染性休克。其他并发症包括肺炎、心律失常、吻合口狭窄、残余狭窄、肉芽肿形成和软化。平均随访时间为 31 个月；4 例患者治愈，1 例需要使用 T 管保持气道通畅。
先天性气管狭窄是一种可治愈的疾病。然而，其修复较为复杂，且与较高的发病率和死亡率相关。
