Canargiu F, Erriu M, Piras A, Dibart S N
Department of Periodontology, University of Cagliari.
Minerva Stomatol. 2009 Jul-Aug;58(7-8):375-81.
Williams syndrome, also known as Williams-Beuren syndrome, or elfin-facies syndrome, was described by Dr. Williams and Dr. Beuren for the first time in 1961 and 1962. This multisystem, congenital and panethnic disorder is characterized by a number of developmental and physical abnormalities like excess of gingiva. The goal of this article is to present the application of a protocol of periodontal treatment leading to the functional rehabilitation of the oral areas affected by excess of gingiva. A 19-year-old boy, diagnosed as suffering from Williams Syndrome, was brought to the dental school, University of Cagliari, seeking for orthodontic and periodontal treatment. During the consultation the excess of gingiva needing periodontal treatment was noticed. This report reveals a classic presentation of the syndrome, with emphasis on its oral and periodontal manifestations. Periodontal management included periodontal flap surgery to treat the excess of gingiva performing clinical crown lengthening. Re-evaluation of the patient after two months showed remarkable reduction of the excess of gingiva. Williams syndrome is clinically important to the periodontist, because of its associated features of excess of gingiva. Periodic examinations are recommended to identify any possible recurrence or complications.
威廉姆斯综合征，也被称为威廉姆斯-贝伦综合征或小精灵面容综合征，于1961年和1962年由威廉姆斯博士和贝伦博士首次描述。这种多系统、先天性且跨越种族的疾病具有多种发育和身体异常特征，比如牙龈增生。本文的目的是介绍一种牙周治疗方案的应用，该方案旨在使受牙龈增生影响的口腔区域实现功能康复。一名19岁男孩被诊断患有威廉姆斯综合征，被带到卡利亚里大学牙科学院寻求正畸和牙周治疗。在会诊期间，发现了需要进行牙周治疗的牙龈增生情况。本报告揭示了该综合征的典型表现，重点关注其口腔和牙周表现。牙周治疗包括进行牙周瓣手术以治疗牙龈增生并实现临床牙冠延长。两个月后对患者的重新评估显示牙龈增生明显减轻。威廉姆斯综合征对牙周病医生具有临床重要性，因为其伴有牙龈增生的相关特征。建议定期检查以发现任何可能的复发或并发症。
