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冯祖布施型银屑病

[Psoriasis of von Zumbusch.

作者信息

Jaime Thais Jerez, Rodrigues Beatriz Alessi, Jaime Tatiana Jerez, Barbo Maria Lourdes Peris, Simis Deborah Regina Cunha

机构信息

Faculdade de Ciências Médicas de Sorocaba, Pontifícia Universidade Católica de São Paulo, Sorocaba, SP, Brazil.

出版信息

An Bras Dermatol. 2009 Jul;84(3):299-301. doi: 10.1590/s0365-05962009000300016.

DOI:10.1590/s0365-05962009000300016
PMID:19668933
Abstract

A disorder of unknown origin, psoriasis is characterized by erythemato-squamous eruption. Amongst its clinical and morphologic presentations there is acute generalized pustular psoriasis, termed the von Zumbusch variant, accompanied by generalized toxicity. It is often triggered when stopping steroids, in unstable psoriasis patients. Case report of atypical development that began during prednisone use; complete clearing of lesions and symptoms was achieved with 35 days of acitretin.

摘要

银屑病是一种病因不明的疾病,其特征为红斑鳞屑性皮疹。在其临床和形态学表现中,有一种急性泛发性脓疱型银屑病,称为冯·祖姆布施型,伴有全身中毒症状。在病情不稳定的银屑病患者中,停用类固醇时常常会引发该病。本文报告了1例在使用泼尼松期间出现非典型病情发展的病例;使用阿维A 35天后,皮损和症状完全消退。

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1
[Psoriasis of von Zumbusch.冯祖布施型银屑病
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2
Successful use of acitretin in conjunction with narrowband ultraviolet B phototherapy in a child with severe pustular psoriasis, von Zumbusch type.阿维A联合窄谱中波紫外线光疗成功治疗1例严重脓疱型银屑病(冯祖布施型)患儿
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Annular pustular psoriasis in a 14-month-old girl: a therapeutic challenge.一名14个月大女童的环状脓疱型银屑病:治疗挑战
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Acitretin.阿维 A 酯。
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Recalcitrant infantile generalized pustular psoriasis successfully treated with acitretin and narrowband ultraviolet B.阿维A和窄谱紫外线B成功治疗顽固性婴儿泛发性脓疱型银屑病
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引用本文的文献

1
Generalized pustular psoriasis induced by systemic steroid dose reduction.系统性类固醇剂量减少诱发的泛发性脓疱型银屑病。
An Bras Dermatol. 2016 Sep-Oct;91(5):664-666. doi: 10.1590/abd1806-4841.20163804.