Nowińska Anna, Wylęgała Edward, Dobrowolski Dariusz
Z Oddziału Okulistycznego Okregowego Szpitala Kolejowego w Katowicach.
Klin Oczna. 2009;111(4-6):153-5.
Posterior polymorphous corneal dystrophy (PPCD) is a rare, bilateral, congenital disorder. It affects endothelial cells and Descemet's membrane. Slit lamp examination of PPCD shows characteristic bilateral endothelial bands, vesicles, and polymorphous opacities at the level of Descemet's membrane and endothelium, which can be accompanied by iridocorneal peripheral adhesions, iris atrophy, and corectopia. The clinical phenotype of PPCD can vary from relatively benign Descemet's thickening to severe progression towards vision loss from corneal edema or consecutive glaucoma. We present a case report of a 7-years old male patient with left eye corneal edema. Diagnosis of PPCD is made by slit-lam examination accompanied by anterior segment optical coherence tomography (AS OCT), and specular microscopy examination. Examination also revealed corneal changes in left eye of 32-years old patient's mother.
后极性多形性角膜营养不良（PPCD）是一种罕见的双侧先天性疾病。它影响内皮细胞和后弹力层。裂隙灯检查PPCD显示后弹力层和内皮水平有特征性的双侧内皮带、水疱和多形性混浊，可伴有虹膜角膜周边粘连、虹膜萎缩和瞳孔异位。PPCD的临床表型可从相对良性的后弹力层增厚到因角膜水肿或继发性青光眼导致视力丧失的严重进展。我们报告一例7岁男性左眼角膜水肿患者。通过裂隙灯检查并结合眼前节光学相干断层扫描（AS OCT）和角膜内皮显微镜检查做出PPCD的诊断。检查还发现32岁患者母亲的左眼有角膜改变。
